Orphanet: Syndrome congenital d hamartome hypothalamique. Request PDF on ResearchGate | On Jul 1, , J. Mounach and others published Puberté précoce liée à un hamartome hypothalamique. Request PDF on ResearchGate | On May 1, , N. Ech-Cherif El Kettani and others published Hamartome hypothalamique révélant des crises gélastiques.

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Routine scalp EEG monitoring and long-term video-EEG monitoring, interictal and ictal 99 m-Tc hexamethylprophyleneamine oxime single photon emission computed tomography SPECTmagnetic resonance imaging MRIneuropsychological evaluation, ophthalmological assessments with perimetry, and endocrinological investigations are included.

hypothalamus hamartome – Translation into English – examples French | Reverso Context

Baizri cH. Furthermore, they did not suggest any treatment strategy for Type 2 sessile HHs.

As the nearby vicinity of HHs consists of very critical structures, the utmost effort should be paid to reduce collateral damage. A proper trajectory directly to HHs and keeping hamartomf disconnection margin straight are essential instructions for minimizing complications.

The relationship between magnetic resonance imaging findings and clinical manifestations of hypothalamic hamartoma. Patients with most unilateral attachment, intraventricular type, and small HHs less than 1.

Endoscopic Treatment of Hypothalamic Hamartomas

Consequently, complete disconnection is considered to be more important than resection. The disconnection will begin at the border between the hamartomas and the mammillary body and proceed along the midline posteroinferior floor of the third ventricle Fig.

Classification and possible treatment selection for hypothalamic hamartoma HH modification from Choi et al. Alternatively, endoscopic surgery, gamma knife surgery, and stereotactic radiofrequency thermo-coagulation have been introduced and presented good outcomes with fewer complications.


The fiberoptic laser or monopolar coagulator is used through the working channel of the hypofhalamique.

Puberté précoce liée à un hamartome hypothalamique – EM|consulte

The mass should not be under the optic tract. Endocrine assessment would include sex hormone and growth hormone levels, thyroid function, prolactin level, and cortisol reserve with glucagon stimulation. Firing behavior and network activity of single neurons in human epileptic hypothalamic hamartoma.

Laguitton aM. After confirmation of the extent of disconnection and seizure outcome, a second disconnection can be performed with fewer complications. hamartomr

Delalande O, Fohlen M. You can move this window by clicking on the headline. More favorable outcomes were guaranteed mostly from near total or total resection If you want to subscribe to this journal, see our rates You can purchase this item in Pay Per View: Endoscopic surgery for hypothalamic ha,artome causing medically refractory gelastic epilepsy.

Neurol Med Chir Tokyo ; Drop attacks and other secondary generalized epilepsy symptoms usually develop as the patient ages. Their classification was based on either pedunculated or sessile sagittal orientation and the treatments included open surgical removal or medicinal intervention.

Complications Transient short-term memory loss, yamartome gain, thalamic infarction with memory loss, and hemiparesis have been reported as early complications.

There should be minimal working space within the third ventricle for forceps and coagulator, as well as definite interface either on the neuronavigational image or direct visualization. Hypothalamic hamartoma, Epilepsy, Endoscope. The owners of this website hereby guarantee to respect the legal confidentiality conditions, applicable in France, and not to disclose this data to third parties.


As per the Law relating to information storage and personal integrity, you have the right to oppose art 26 of that lawaccess art 34 of that law and rectify art 36 of that law your personal hamrtome.

However, surgical resection for total removal of HHs have led to good seizure outcomes and behavioral improvement 10 Access to the full text of this article requires a subscription.

The direction of dissection around the lateral border of HHs. Open in a separate window. Acceptable morbidity has made multiple-staged operations possible 2431 Surgical indications are intractable GS, neurobehavioral deterioration, and the absence of a cortical lesion on MRI.

The depth electrode will guide the disconnection surgery as well as confirm the successful disconnection 28 This rare non-neoplastic abnormal mixture of neuronal and glial tissue of the inferior hypothalamus has been postulated to be derived from the mammillo-thalamo-cingulate tract from which HH is networking other brain areas associated with GS or the pathway from the HH to hamartlme brainstem and cerebellum 16 Access to the text HTML.

Top of the page – Article Outline. Endoscopic disconnection has been one of the most favorable options performed in treating HHs. You may thus request that your data, should it be inaccurate, incomplete, unclear, outdated, not be used or stored, be corrected, clarified, updated or deleted.